Peds, part 23: Cardiovascular Disorders - Congenital Heart Defects - ASD, VSD, AV Canal, PDA, Tetralogy of Fallot, Tricuspid Atresia

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In this article and video, we cover pediatric congenital heart defects that increase pulmonary blood flow, as well as those that decrease pulmonary blood flow.

This series follows along with our Pediatric Nursing - Flashcards which are intended to help RN and PN nursing students study for nursing school exams, including the ATI, HESI, and NCLEX.

Congenital heart defects leading to increased pulmonary blood flow

Congenital heart defects that increase pulmonary blood flow include the atrial septal defect, a ventricular septal defect, an atrioventricular canal defect, and a patent ductus arteriosus.

Atrial septal defect

An atrial septal defect (ASD) is a congenital heart defect where a hole in the septum separates the left and right atria of the heart. An ASD leads to increased pulmonary blood flow.

Patients with this type of defect may be asymptomatic, but it can also cause signs and symptoms of heart failure as well as a murmur.

This murmur will be a systolic murmur with a wide, fixed splitting of S2.

Treatment options for ASD include closure with cardiac catheterization and surgical patch closure.

Ventricular septal defect

A ventricular septal defect (VSD) is a congenital heart defect where there is a hole in the septum that separates the left and right ventricles of the heart. So it's the same concept as ASD described above, but the hole is between the ventricles rather than the atria. VSD leads to increased pulmonary blood flow.

Signs and symptoms of VSD include signs and symptoms of heart failure as well as a murmur. This murmur can be described as a loud systolic murmur at the left sternal border.

Treatment options for VSD include surgery to suture or patch the hole.

Atrioventricular canal

An atrioventricular canal (AV canal) defect is a congenital heart defect where there is a large hole in the center of the heart that allows blood to flow between all four chambers of the heart. Instead of a mitral valve and a tricuspid valve, patients with an AV canal defect have a single AV valve. An AV canal defect leads to increased pulmonary blood flow.

An AV canal defect can cause signs and symptoms of heart failure as well as a loud systolic murmur.

Treatment options for an AV canal defect include surgical patch closure, as well as valve reconstruction.

Patent ductus arteriosus

A patent ductus arteriosus (PDA) defect is a congenital heart defect where the fetal artery that connects the aorta to the pulmonary artery fails to close after birth. A PDA defect can cause signs and symptoms like a machine hum murmur, bounding pulses, and a wide pulse pressure (a large difference between the systolic blood pressure and the diastolic blood pressure). PDA leads to increased pulmonary blood flow.

Treatment for a PDA defect can include the use of indomethacin, which is an NSAID, and using coils to occlude the PDA during cardiac catheterization. Indomethacin and other cardiac meds are covered in detail in our Pharmacology - Nursing Flashcards

Cool Chicken INdomethacin goes IN da hole and closes it!

A story from Cathy on how to remember PDA symptoms and treatment

Another little story that may be helpful for you to remember some of the signs and symptoms of this congenital heart defect, if you look at PDA, that also stands for public displays of affection. So I imagine a dad looking out his window and seeing his daughter engaging in PDA with a boy he really doesn't like, and that causes him to have bounding pulses. And he wished he had a machine gun, which he doesn't have, and he opens up the window and he yells, "Get in here." So this little story will help you remember, with PDA, that it will cause bounding pulses, a machine hum murmur, and that Indomethacin is used to treat it. When he yells, "Get in here," that will help you to remember Indomethacin. So hopefully, that little story helps.

Congenital heart defects leading to decreased pulmonary blood flow

Congenital heart defects that lead to decreased pulmonary blood flow include tetralogy of Fallot, and tricuspid atresia.

Tetralogy of Fallot

Tetralogy of Fallot (TOF) is a congenital heart defect comprising four different defects: pulmonary stenosis, right ventricular hypertrophy, overriding aorta, and ventricular septal defect. Tetralogy of Fallot causes decreased pulmonary blood flow. You can remember that it's made up of four defects by knowing that the tetra- prefix means four.

Cool Chicken PROVE that you know all 4!: Pulmonary Stenosis, Right Ventricular Hypertrophy, Overriding Aorta, Ventricular Septal Defect, Excellent you got all four!

Signs and symptoms of TOF include cyanosis (the child may have hypercyanotic or "tet" spells). To address cyanosis, you should place the patient in a knee-chest position in order to increase blood flow to the lungs. In addition, the patient may have a systolic murmur present.

Treatment for TOF includes surgical repair within the first year of life.

Tricuspid atresia

Tricuspid atresia is a congenital heart defect where the tricuspid valve, which normally separates the right atrium from the right ventricle, fails to develop, and blood flows through a ventricular septal defect or an atrial septal defect. Tricuspid atresia causes decreased pulmonary blood flow.

Signs and symptoms of tricuspid atresia include cyanosis, tachycardia, dyspnea, as well as clubbing (upside-down, spoon-shaped nails) indicative of hypoxia.

Treatment of tricuspid atresia can require multiple surgeries, including shunt placement, a Glenn procedure, and a Fontan procedure.

Quiz Questions

With a ventricular septal defect, where is the heart murmur heard?

At the left sternal border

Which congenital heart defect is characterized by a machine hum murmur and bounding pulses?

Patent ductus arteriosus

For hypercyanotic episodes associated with tetralogy of Fallot, how do you position the child?

In a knee-chest position

Full Transcript: Peds, part 23: Cardiovascular Disorders - Congenital Heart Defects - ASD, VSD, AV Canal, PDA, Tetralogy of Fallot, Tricuspid Atresia

Hi, I'm Cathy, with Level Up RN. In this video, we are going to talk about congenital heart defects that increase pulmonary blood flow, as well as those that decrease pulmonary blood flow. At the end of the video, I'm going to give you guys a little quiz to test your knowledge of some of the key points I'll be covering in this video. And if you have our Level Up RN pediatric nursing flashcards, definitely pull those out so you can follow along with me, and pay close attention to the bold red items on these cards because there are a lot of important points you have to know about these congenital heart defects.

Let's start off by talking about defects that cause increased pulmonary blood flow. This includes an atrial septal defect, or ASD, a ventricular septal defect, or VSD, an AV canal defect, as well as a patent ductus arteriosus, or PDA defect.

So with ASD, an atrial septal defect, this is where we have a hole in the septum that separates the left and right atria.

Patients with this type of defect may be asymptomatic, but it can also cause signs and symptoms of heart failure as well as a murmur. So this murmur will be a systolic murmur with a wide fix splitting of S2.

Treatment options include closure with cardiac catheterization as well as surgical patch closure.

With a ventricular septal defect, or VSD, this is where we have a hole in the septum between the left and right ventricles.

Signs and symptoms include signs and symptoms of heart failure as well as a murmur. This murmur can be described as a loud systolic murmur at the left sternal border.

Treatment options for VSD include surgery to suture or patch the hole.

With an AV canal defect, we have basically a hole in the center of the heart that allows blood to flow between all four chambers.

Instead of a mitral valve and a tricuspid valve, we have a single AV valve, and this can cause signs and symptoms of heart failure as well as a loud systolic murmur.

Treatment includes surgical patch closure as well as valve reconstruction.

And then the last congenital heart defect that results in increased pulmonary blood flow is a PDA, or patent ductus arteriosus. So this is where the fetal artery that connects the aorta to the pulmonary artery fails to close after birth.

And this can cause signs and symptoms such as a machine hum murmur, bounding pulses, and a wide pulse pressure, meaning that we have a big difference between the systolic blood pressure and the diastolic blood pressure.

Treatment can include the use of Indomethacin, which is an NSAID. It can also include using coils to occlude the PDA during cardiac catheterization. A little cool chicken hint here at the bottom of the card is Indomethacin goes in the hole and closes it.

Another little story that may be helpful for you to remember some of the signs and symptoms of this congenital heart defect, if you look at PDA, that also stands for public displays of affection. So I imagine a dad looking out his window and seeing his daughter engaging in PDA with a boy he really doesn't like, and that causes him to have bounding pulses. And he wished he had a machine gun, which he doesn't have, and he opens up the window and he yells, "Get in here." So this little story will help you remember, with PDA, that will cause bounding pulses, a machine hum murmur, and that Indomethacin is used to treat it. When he yells, "Get in here," that will help you to remember Indomethacin. So hopefully, that little story helps.

Let's talk about congenital heart defects that result in decreased pulmonary blood flow.

The first to know is tetralogy of Fallot, or TOF. This is actually a combination of four different defects.

And we have a cool chicken hint here on the card to help you remember those four defects. So the cool chicken hint states, "Prove that you know all four." So with prove, the P stands for pulmonary stenosis, the R stands for right ventricular hypertrophy, the O stands for overriding aorta, and the V stands for ventricular septal defect, and the E doesn't stand for anything. It just stands for, "Excellent. You got the other four right."

So that's our little trick to remember those four.

Signs and symptoms of this defect include cyanosis. So the child may have hypercyanotic or tet spells.

And to address those, you should place the patient in a knee-chest position in order to increase blood flow to the lungs.

In addition, the patient may have a systolic murmur present.

Treatment includes surgical repair within the first year of life.

Then, the second condition that causes decreased pulmonary blood flow is tricuspid atresia. This is where the tricuspid valve, which normally separates the right atrium from the right ventricle, fails to develop and blood flows through a ventricular septal defect or an atrial septal defect.

So signs and symptoms include cyanosis, tachycardia, dyspnea, as well as clubbing. So clubbing is where we have those upside down spoon-shaped nails, which are indicative of hypoxia.

So treatment of this condition requires multiple surgeries, which include shunt placement, a glen procedure, and a Fontan procedure.

All right. It's quiz time. I have three questions for you.

First question, with a ventricular septal defect, where is the murmur heard?

The answer is at the left sternal border

Question number two, which congenital heart defect is characterized by a machine hum murmur and bounding pulses?

The answer is a PDA or patent ductus arterios.

Question number three, for hypercyanotic episodes associated with tetralogy of Fallot, how do you position the child?

The answer is in a knee-chest position.

All right. I hope we did well with that quiz. I hope this video and our cards are helpful. In my next video, we will talk about congenital heart defects that result in obstruction of blood flow and mixed blood flow. So definitely stay tuned for that.

And if you enjoyed this video and learned a lot, be sure to like the video and leave me a comment. Take care and good luck studying.

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